KERATOZA DISEMINATA CIRCUMSCRISA
kbratose disse-minee circonscrite / dyskeratosis congenita. Distrofie con-genitala si familiala (cu transmitere dominants) caracterizata prin papule oomoase foliculare confluente, asodate cu keratoder-mie palmoplantara, pahionichie, leucokeratoza bucala, kerati-nizari corneene si tulburari psihice. Sin.: boala Jadassohn-Lewandowsky, pahionichie congenitala.